Eagle Barrett Syndrome (Also Known as Prune-Belly Syndrome [PBS]) in an Adult

Christopher Wen, MD; Dorothy J. Marquez, MD; Allen J. Cohen, PhD, MD

Disclosures

Appl Radiol. 2004;33(4) 

In This Article

Treatment and Prognosis

The prognosis depends on the severity of the abnormalities. The presentation can range from stillborn fetuses to older children with recurrent infections and renal insufficiency. Orchiopexy is required due to the increased risk of malignancy in undescended testes. Repair of the abdominal wall musculature is not simply cosmetic, as it plays an important role in pulmonary, bladder, and intestinal function and is crucial in the surgical management of these patients.[4]

The diagnosis of PBS should be made in an adult whose CT scans show renal hypoplasia, hydronephrosis, redundant hydroureter, and deficient anterior abdominal musculature.

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