Eagle Barrett Syndrome (Also Known as Prune-Belly Syndrome [PBS]) in an Adult

Christopher Wen, MD; Dorothy J. Marquez, MD; Allen J. Cohen, PhD, MD


Appl Radiol. 2004;33(4) 

In This Article

Treatment and Prognosis

The prognosis depends on the severity of the abnormalities. The presentation can range from stillborn fetuses to older children with recurrent infections and renal insufficiency. Orchiopexy is required due to the increased risk of malignancy in undescended testes. Repair of the abdominal wall musculature is not simply cosmetic, as it plays an important role in pulmonary, bladder, and intestinal function and is crucial in the surgical management of these patients.[4]

The diagnosis of PBS should be made in an adult whose CT scans show renal hypoplasia, hydronephrosis, redundant hydroureter, and deficient anterior abdominal musculature.


Comments on Medscape are moderated and should be professional in tone and on topic. You must declare any conflicts of interest related to your comments and responses. Please see our Commenting Guide for further information. We reserve the right to remove posts at our sole discretion.