What are the possible complications of secondary congenital glaucoma in patients with Sturge-Weber syndrome (encephalofacial angiomatosis)?

Updated: Jul 27, 2020
  • Author: Inci Irak Dersu, MD, MPH; Chief Editor: Hampton Roy, Sr, MD  more...
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Sturge-Weber syndrome (encephalofacial angiomatosis)

These eyes carry high risk for expulsive choroidal hemorrhage upon entering the eye causing sudden pressure change.

They are more likely to develop choroidal effusion from choroidal cavernous hemangioma.

Reducing the IOP as low as possible and performing posterior sclerotomies prior to entering the eye may reduce complications.

In a study by Iwach et al, intraoperative choroidal expansion was detected in 24% of patients who underwent trabeculectomy. [6]

In Agarwal's series of 18 patients with Sturge-Weber syndrome who underwent the trabeculotomy-trabeculectomy procedure, the following complications were noted: intraoperative hyphema (22.2%), vitreous loss (16.7%), and vitreous hemorrhage (5.6%). [5]

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