What causes acquired angioedema (AAE) due to C1 inhibitor (C1-INH) deficiency (C1-INH-AAE) type I?

Updated: May 20, 2020
  • Author: Amanda T Moon, MD; Chief Editor: William D James, MD  more...
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Acquired angioedema type I is most frequently associated with B-cell lymphoproliferative disease. To date, only three reports of a T-cell lymphoma associated with acquired angioedema type I have been documented. [5]

Other associated disorders have included the following:

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